
Ewing's sarcoma (ES) is the 2nd primary bone tumor of childhood, mostly located in the lower extremities. The incidence of primary cranial ES is <1%. Our patient is 9 years old female who has intracranial primary ES extending from the sphenoid bone corpus to the clivus border. This is a rare case of childhood that's originating from the sphenoid bone and spreading to such a very large intracranial area. Our aim is to provide data on the clinical and therapeutic course of a rare case.